


{"id":7835,"date":"2025-07-02T03:24:40","date_gmt":"2025-07-01T19:24:40","guid":{"rendered":"https:\/\/allcancer.com\/cancer\/pleuropulmonary-blastoma-ppb-2\/"},"modified":"2025-07-02T11:22:51","modified_gmt":"2025-07-02T03:22:51","slug":"%e8%83%b8%e8%86%9c%e8%82%ba%e6%b3%a1%e7%98%a4-ppb-%e7%99%8c%e7%97%87","status":"publish","type":"cancer_type","link":"https:\/\/allcancer.com\/hk\/%e7%99%8c%e7%97%87\/%e8%83%b8%e8%86%9c%e8%82%ba%e6%b3%a1%e7%98%a4-ppb-%e7%99%8c%e7%97%87\/","title":{"rendered":"\u80f8\u819c\u80ba\u6bcd\u7ec6\u80de\u7624 (PPB)"},"content":{"rendered":"<h2 class=\"h2-cancertype\">\u4ec0\u9ebc\u662f <strong>\u80f8\u819c\u80ba\u6bcd\u7ec6\u80de\u7624 (PPB)<\/strong>?<\/h2>\n<p class=\"p-cancertype\">Pleuropulmonary Blastoma (PPB) \u662f\u4e00\u7a2e\u7f55\u898b\u7684\u4fb5\u8972\u6027\u5c0f\u5152\u764c\u75c7\uff0c\u8d77\u6e90\u65bc\u80ba\u90e8\u548c\u80f8\u819c\uff0c\u4e3b\u8981\u5f71\u97ff\u516d\u6b72\u4ee5\u4e0b\u7684\u5152\u7ae5\u3002\u8207\u5178\u578b\u7684\u6210\u4eba\u80ba\u764c\u4e0d\u540c\uff0cPPB \u662f\u4e00\u7a2e\u7368\u7279\u7684\u80ba\u90e8\u816b\u7624\uff0c\u7279\u5fb5\u70ba\u539f\u59cb\u7684\u80da\u82bd\u7d30\u80de\u548c\u8089\u7624\u7d30\u80de\u3002\u77ad\u89e3 <strong>\u80f8\u819c\u80ba\u6bcd\u7ec6\u80de\u7624 (PPB)<\/strong> \u662f\u65e9\u671f\u8a3a\u65b7\u548c\u6539\u5584\u7ba1\u7406\u7d50\u679c\u7684\u95dc\u9375\u3002<\/p>\n<p class=\"p-cancertype\">PPB \u4e2d\u7684\u764c\u7d30\u80de\u986f\u793a\u51fa\u660e\u986f\u7684\u4ee3\u8b1d\u8106\u5f31\u6027\uff0c\u7279\u5225\u662f\u5176\u5c0d\u8461\u8404\u7cd6\u4ee3\u8b1d\u7684\u4f9d\u8cf4\uff0c\u5373\u6240\u8b02\u7684\u6c83\u4f2f\u683c\u6548\u61c9\uff08Warburg effect\uff09\u3002\u9019\u7a2e\u73fe\u8c61\u53cd\u6620\u51fa PPB \u7d30\u80de\u5373\u4f7f\u5728\u6709\u5145\u8db3\u6c27\u6c23\u7684\u60c5\u6cc1\u4e0b\uff0c\u4e5f\u50be\u5411\u65bc\u512a\u5148\u9032\u884c\u8461\u8404\u7cd6\u7684\u7121\u6c27\u4ee3\u8b1d\uff0c\u5176\u4ee3\u8b1d\u901f\u5ea6\u6709\u6642\u6bd4\u6b63\u5e38\u7d30\u80de\u9ad8\u51fa 200 \u500d\uff0c\u56e0\u6b64\u6210\u70ba\u5275\u65b0\u4ee3\u8b1d\u7642\u6cd5\u7684\u6f5b\u5728\u76ee\u6a19\u3002<\/p>\n<p class=\"p-cancertype\">\u6839\u64da\u4e16\u754c\u885b\u751f\u7d44\u7e54(2024)\u7684\u7d71\u8a08\uff0c\u5168\u7403\u6bcf\u5e74\u7d04\u6709220\u842c\u4eba\u7f79\u60a3\u80ba\u764c\u3002\u5118\u7ba1 PPB \u53ea\u4f54\u6574\u9ad4\u767c\u75c5\u7387\u7684\u6975\u5c0f\u90e8\u5206\uff0c\u4f46\u5b83\u5c0d\u5305\u62ec\u9999\u6e2f\u5728\u5167\u7684\u5730\u5340\u7684\u5152\u79d1\u5065\u5eb7\u7684\u5f71\u97ff\uff0c\u9700\u8981\u81f4\u529b\u65bc\u816b\u7624\u5b78\u7684\u91ab\u5b78\u7814\u7a76\u4eba\u54e1\u548c\u81e8\u5e8a\u91ab\u751f\u5bc6\u5207\u95dc\u6ce8\u3002<\/p>\n<p class=\"p-cancertype\">PPB \u901a\u5e38\u5206\u70ba\u4e09\u500b\u968e\u6bb5\uff1aI \u578b\uff08\u7d14\u7cb9\u56ca\u6027\uff0c\u901a\u5e38\u662f\u6700\u65e9\u7684\u968e\u6bb5\uff09\u3001II \u578b\uff08\u7d50\u5408\u56ca\u6027\u548c\u5be6\u6027\uff09\u548c III \u578b\uff08\u5b8c\u5168\u5be6\u6027\uff0c\u6700\u5177\u4fb5\u8972\u6027\uff09\u3002\u53ca\u65e9\u767c\u73fe\u53ef\u5927\u5927\u63d0\u9ad8\u6cbb\u7642\u6548\u679c\uff0c\u56e0\u6b64\u5f37\u8abf\u5728\u516c\u773e\u548c\u81e8\u5e8a\u9818\u57df\u4e2d\u63d0\u9ad8\u610f\u8b58\u7684\u91cd\u8981\u6027\uff0c\u5c24\u5176\u662f\u5728\u4eba\u53e3\u7a20\u5bc6\u7684\u57ce\u5e02\uff0c\u5982\u9999\u6e2f\u3002<\/p>\n<h3 class=\"h3-cancertype\">\u53d7\u5f71\u97ff\u4eba\u53e3\u53ca\u5730\u5340\u6578\u64da\uff08\u4e9e\u6d32\u53ca\u9999\u6e2f\uff09<\/h3>\n<p class=\"p-cancertype\">Pleuropulmonary Blastoma (PPB) \u4e3b\u8981\u5f71\u97ff\u5e74\u5e7c\u5152\u7ae5\uff0c\u901a\u5e38\u5728\u516d\u6b72\u524d\u8a3a\u65b7\uff0c\u56e0\u6b64\u65e9\u671f\u5152\u79d1\u8a3a\u65b7\u662f\u95dc\u9375\u56e0\u7d20\u3002\u6d41\u884c\u75c5\u5b78\u7d71\u8a08\u8cc7\u6599\u986f\u793a\uff0c\u5168\u7403\u7d04\u6709 50% \u7684\u8a3a\u65b7\u5c0d\u8c61\u521d\u671f\u70ba PPB I \u578b\uff0c\u8207\u665a\u671f\u578b\u614b\u76f8\u6bd4\uff0c\u60a3\u8005\u7684\u7642\u6548\u986f\u8457\u589e\u52a0\u3002<\/p>\n<p class=\"p-cancertype\">\u5728\u9999\u6e2f\uff0c\u7576\u5730\u7684\u5065\u5eb7\u6578\u64da\u986f\u793a\uff0c\u5305\u62ec PPB \u7b49\u7f55\u898b\u764c\u75c7\u5728\u5167\u7684\u5152\u7ae5\u764c\u75c7\u9700\u8981\u5c08\u9580\u7684\u8b77\u7406\u8a2d\u65bd\u548c\u6cbb\u7642\u3002\u8207\u6df1\u5733\u524d\u6d77\u6cf0\u5eb7\u548c MD Anderson \u7b49\u6a5f\u69cb\u5408\u4f5c\u9032\u884c\u7684\u907a\u50b3\u5b78\u7814\u7a76\uff0c\u6709\u52a9\u65bc\u77ad\u89e3\u5730\u5340\u6613\u611f\u6027\u548c\u6cbb\u7642\u9032\u5c55\uff0c\u8207\u570b\u969b\u816b\u7624\u5b78\u7814\u7a76\u6a19\u6e96\u7dca\u5bc6\u63a5\u8ecc\u3002<\/p>\n<ul class=\"p-cancertype\">\n<li>\u5168\u7403\u767c\u75c5\u7387\u4ecd\u5c6c\u7f55\u898b\uff0c\u7a81\u986f\u51fa\u5c08\u696d\u77e5\u8b58\u548c\u5927\u773e\u610f\u8b58\u7684\u91cd\u8981\u6027\u3002<\/li>\n<li>\u4e9e\u6d32\u4eba\u53e3\uff0c\u5c24\u5176\u662f\u50cf\u9999\u6e2f\u9019\u6a23\u90fd\u5e02\u5bc6\u96c6\u7684\u5730\u5340\uff0c\u9700\u8981\u8b66\u89ba\u6027\u9ad8\u7684\u5152\u79d1\u816b\u7624\u57fa\u790e\u8a2d\u65bd\u548c\u652f\u63f4\u6027\u7684\u5bb6\u5ead\u670d\u52d9\u3002<\/li>\n<li>\u5bb6\u5ead\u6240\u9762\u81e8\u7684\u5fc3\u7406\u548c\u751f\u7406\u6311\u6230\u53ef\u80fd\u975e\u5e38\u6df1\u9060\uff0c\u9019\u9032\u4e00\u6b65\u5f37\u5316\u4e86\u53ca\u6642\u3001\u9ad4\u6064\u548c\u5168\u9762\u6cbb\u7642\u65b9\u6cd5\u7684\u5fc5\u8981\u6027\u3002<\/li>\n<\/ul>\n<p class=\"p-cancertype\">\u9032\u4e00\u6b65\u4e86\u89e3\u6211\u5011\u7684 <a href=\"\/hk\/cancer-biology\/\" target=\"_blank\" rel=\"noopener\">\u764c\u75c7\u751f\u7269\u5b78<\/a> \u9801\u9762\u6216\u6211\u5011\u5275\u65b0\u7684 <a href=\"\/hk\/diagnostics\/\" target=\"_blank\" rel=\"noopener\">\u8a3a\u65b7\u65b9\u6cd5<\/a>\u8a72\u8a08\u5283\u65e8\u5728\u65e9\u671f\u8b58\u5225\u548c\u7ba1\u7406\u7f55\u898b\u7684\u5152\u79d1\u816b\u7624\uff0c\u5982\u80f8\u80ba\u6bcd\u7d30\u80de\u7624 (PPB)\u3002<\/p>\n<h2 class=\"h2-cancertype\">\u80f8\u819c\u80ba\u6bcd\u7d30\u80de\u7624 (PPB) \u7684\u6210\u56e0\u8207\u98a8\u96aa\u56e0\u7d20<\/h2>\n<p class=\"p-cancertype\">\u4e86\u89e3 Pleuropulmonary Blastoma (PPB) \u7684\u75c5\u56e0\u5c0d\u65bc\u6709\u6548\u7684\u6cbb\u7642\u548c\u9810\u9632\u6709\u5f88\u5927\u7684\u5e6b\u52a9\u3002\u8207\u8a31\u591a\u5152\u7ae5\u764c\u75c7\u4e00\u6a23\uff0cPPB \u6d89\u53ca\u8907\u96dc\u7684\u907a\u50b3\u3001\u74b0\u5883\u548c\u65b0\u9673\u4ee3\u8b1d\u76f8\u4e92\u4f5c\u7528\uff0c\u5c0d\u6d41\u884c\u75c5\u5b78\u5bb6\u548c\u5c08\u5bb6\u90fd\u662f\u4e00\u5927\u6311\u6230\u3002<\/p>\n<h3 class=\"h3-cancertype\">PPB \u767c\u80b2\u904e\u7a0b\u4e2d\u7684\u907a\u50b3\u56e0\u7d20<\/h3>\n<p class=\"p-cancertype\">Pleuropulmonary Blastoma\uff08PPB\uff09\u7684\u907a\u50b3\u5f71\u97ff\u4e3b\u8981\u8207 DICER1 \u57fa\u56e0\u7a81\u8b8a\u6709\u95dc\uff0c\u5728\u7d04 70% \u7684\u75c5\u4f8b\u4e2d\u53ef\u898b\u5230\u9019\u7a2e\u7a81\u8b8a\u3002DICER1 \u57fa\u56e0\u7a81\u8b8a\u6703\u64fe\u4e82 microRNA \u7684\u8655\u7406\uff0c\u5f71\u97ff\u6b63\u5e38\u7684\u7d30\u80de\u589e\u6b96\u548c\u5206\u5316\uff0c\u4f7f\u5152\u7ae5\u5bb9\u6613\u7f79\u60a3 PPB\u3002<\/p>\n<ul class=\"p-cancertype\">\n<li>\u5728\u5bb6\u65cf\u75c5\u4f8b\u548c\u500b\u5225\u75c5\u4f8b\u4e2d\u767c\u73fe DICER1 \u57fa\u56e0\u7a81\u8b8a\uff0c\u7a81\u986f\u907a\u50b3\u8aee\u8a62\u7684\u5fc5\u8981\u6027\u3002<\/li>\n<li>\u5efa\u8b70\u53ca\u65e9\u9032\u884c\u57fa\u56e0\u7be9\u6aa2\uff0c\u5c24\u5176\u662f\u5df2\u78ba\u8a3a\u75c5\u60a3\u7684\u5144\u5f1f\u59ca\u59b9\u6216\u5f8c\u4ee3\u3002<\/li>\n<li>MD Anderson \u7b49\u7814\u7a76\u6a5f\u69cb\u7684\u6700\u65b0\u7814\u7a76\u9032\u4e00\u6b65\u5f37\u8abf\u7cbe\u6e96\u57fa\u56e0\u7814\u7a76\uff0c\u4f7f\u65e9\u671f\u4ecb\u5165\u548c\u500b\u4eba\u5316\u6cbb\u7642\u6210\u70ba\u53ef\u80fd\u3002<\/li>\n<\/ul>\n<h3 class=\"h3-cancertype\">\u74b0\u5883\u5f71\u97ff\u8207\u5152\u79d1\u816b\u7624\u5b78<\/h3>\n<p class=\"p-cancertype\">\u8207\u6210\u4eba\u80ba\u90e8\u60e1\u6027\u816b\u7624 (\u5982\u8207\u5438\u7159\u6709\u95dc\u7684\u80ba\u764c) \u76f8\u6bd4\uff0c\u5c0e\u81f4\u80f8\u819c\u80ba\u6ce1\u7624 (PPB) \u7684\u74b0\u5883\u63a5\u89f8\u4ecd\u6c92\u6709\u90a3\u9ebc\u7cbe\u78ba\u7684\u5b9a\u7fa9\u3002\u7136\u800c\uff0c\u67d0\u4e9b\u574a\u9593\u7814\u7a76\u986f\u793a\uff0c\u74b0\u5883\u81f4\u764c\u7269\u6216\u7522\u524d\u66b4\u9732\u53ef\u80fd\u6703\u7a0d\u5fae\u589e\u52a0\u5c0f\u5152\u816b\u7624\u98a8\u96aa\u3002<\/p>\n<ul class=\"p-cancertype\">\n<li>\u6709\u9650\u7684\u8b49\u64da\u986f\u793a\uff0c\u7522\u524d\u63a5\u89f8\u67d0\u4e9b\u6bd2\u7d20\u6216\u81f4\u764c\u7269\u8207\u7f55\u898b\u7684\u5152\u79d1\u764c\u75c7\u6709\u95dc\u3002<\/li>\n<li>\u76ee\u524d\u6b63\u5728\u9032\u884c\u5ee3\u6cdb\u7684\u7814\u7a76\uff0c\u4ee5\u91d0\u6e05\u5305\u62ec PPB \u5728\u5167\u7684\u5152\u79d1\u816b\u7624\u7684\u74b0\u5883-\u907a\u50b3\u4ea4\u4e92\u4f5c\u7528\u3002<\/li>\n<li>\u61c9\u7e7c\u7e8c\u52a0\u5f37\u5f37\u8abf\u7522\u524d\u4fdd\u5065\u548c\u6e1b\u5c11\u63a5\u89f8\u7684\u516c\u5171\u5065\u5eb7\u610f\u8b58\u6d3b\u52d5\u3002<\/li>\n<\/ul>\n<h3 class=\"h3-cancertype\">\u4ee3\u8b1d\u8106\u5f31\u6027\uff1a\u5c08\u6ce8\u65bc\u8461\u8404\u7cd6\u548c\u8c37\u6c28\u9170\u80fa<\/h3>\n<p class=\"p-cancertype\">\u5728\u764c\u75c7\u751f\u7269\u5b78\u4e2d\u89c0\u5bdf\u5230\u7684\u4ee3\u8b1d\u4f9d\u8cf4\u6027\u5c55\u793a\u4e86\u6cbb\u7642\u7684\u6f5b\u529b\u3002Pleuropulmonary Blastoma (PPB) \u4e3b\u8981\u5229\u7528\u8461\u8404\u7cd6\u4ee3\u8b1d\uff08\u6c83\u4f2f\u683c\u6548\u61c9\uff09\uff0c\u5076\u723e\u4e5f\u6703\u5229\u7528\u8c37\u6c28\u9170\u80fa\u4f86\u9032\u884c\u5feb\u901f\u7684\u7d30\u80de\u589e\u6b96\u3001\u6838\u82f7\u9178\u5408\u6210\u4ee5\u53ca\u7dda\u7c92\u9ad4\u751f\u7269\u80fd\u3002<\/p>\n<ul class=\"p-cancertype\">\n<li>PPB \u7d30\u80de\u6d88\u8017\u8461\u8404\u7cd6\u7684\u901f\u5ea6\u6bd4\u6b63\u5e38\u7d30\u80de\u5feb 200 \u500d\uff0c\u63d0\u4f9b\u4e86\u91dd\u5c0d\u6027\u65b0\u9673\u4ee3\u8b1d\u6cbb\u7642\u7684\u6a5f\u6703\u3002<\/li>\n<li>\u5305\u62ec\u8afe\u8c9d\u723e\u734e\u5f97\u4e3b Gregg Semenza \u5728\u5167\u7684\u9802\u5c16\u4eba\u7269\u7684\u7814\u7a76\u8aaa\u660e\uff0c\u91dd\u5c0d\u65b0\u9673\u4ee3\u8b1d\u7684\u5f31\u9ede\u53ef\u4ee5\u986f\u8457\u6539\u8b8a PPB \u7684\u7ba1\u7406\uff0c\u5305\u62ec\u5be6\u9a57\u6027\u7684\u65b0\u9673\u4ee3\u8b1d\u6291\u5236\u5291\u548c\u98f2\u98df\u5e72\u9810\u3002<\/li>\n<li>\u5275\u65b0\u7684\u4ee3\u8b1d\u764c\u75c7\u7642\u6cd5\uff0c\u4f8b\u5982\u816b\u7624\u5b78\u5c08\u5bb6\u674e\u570b\u83ef\u535a\u58eb\u548c\u5289\u570b\u9f8d\u6559\u6388\u6240\u958b\u767c\u7684\u7642\u6cd5\uff0c\u70ba\u9999\u6e2f\u548c\u6574\u500b\u4e9e\u6d32\u63d0\u4f9b\u5148\u9032\u7684\u6cbb\u7642\u65b9\u6848\u92ea\u8def\u3002<\/li>\n<\/ul>\n<h3 class=\"h3-cancertype\">\u9810\u9632\u63aa\u65bd\u8207\u65e9\u671f\u5075\u6e2c\u7b56\u7565<\/h3>\n<p class=\"p-cancertype\">\u9451\u65bc\u907a\u50b3\u50be\u5411\u7684\u76f8\u95dc\u6027\uff0cDICER1 \u57fa\u56e0\u7a81\u8b8a\u7684\u65e9\u671f\u57fa\u56e0\u7be9\u6aa2\u53ef\u5c0d\u7d50\u679c\u7522\u751f\u6df1\u9060\u7684\u5f71\u97ff\uff0c\u4e26\u53ef\u9032\u884c\u9810\u9632\u6027\u5e72\u9810\u53ca\u5bc6\u5207\u76e3\u6e2c\u3002\u8f14\u52a9\u6027\u7684\u751f\u6d3b\u65b9\u5f0f\u5efa\u8b70\u548c\u5152\u79d1\u816b\u7624\u5c08\u5bb6\u7684\u5b9a\u671f\u8ffd\u8e64\u8a3a\u65b7\u81f3\u95dc\u91cd\u8981\u3002<\/p>\n<ul class=\"p-cancertype\">\n<li>\u63d0\u5021\u5c0d\u6d89\u53ca DICER1 \u7684\u53ef\u7591\u5bb6\u65cf\u75c5\u4f8b\u9032\u884c\u57fa\u56e0\u6e2c\u8a66\u3002<\/li>\n<li>\u5728\u9999\u6e2f\u548c\u66f4\u5ee3\u6cdb\u7684\u4e9e\u6d32\u793e\u5340\u63a8\u52d5\u8a8d\u77e5\u6d3b\u52d5\uff0c\u8457\u91cd\u65bc\u8b58\u5225\u65e9\u671f\u75c7\u72c0\u3002<\/li>\n<li>\u4fc3\u9032\u5340\u57df\u5408\u4f5c\uff08\u5982\u6df1\u5733\u524d\u6d77\u6cf0\u5eb7\uff09\uff0c\u70ba\u9ad8\u98a8\u96aa\u5bb6\u5ead\u63d0\u4f9b\u65b9\u4fbf\u7684\u7be9\u67e5\u8a08\u5283\u548c\u5148\u9032\u7684\u8a3a\u65b7\u65b9\u6cd5\u3002<\/li>\n<\/ul>\n<p class=\"p-cancertype\">\u63a2\u7d22\u6211\u5011\u7684 <a href=\"\/hk\/core-therapies\/\" target=\"_blank\" rel=\"noopener\">\u6838\u5fc3\u6cbb\u7642<\/a> \u9801\u9762\u767c\u73fe\u9769\u547d\u6027\u7684\u65b0\u9673\u4ee3\u8b1d\u816b\u7624\u5b78\u7642\u6cd5\uff0c\u6539\u8b8a\u5c0f\u5152\u764c\u75c7\u7167\u8b77\uff0c\u6709\u6548\u4e14\u6709\u611b\u5fc3\u5730\u89e3\u6c7apleasuraly blastboma \u7684\u65b0\u9673\u4ee3\u8b1d\u5f31\u9ede\u3002<\/p>\n<h2 class=\"h2-cancertype\">Pleuropulmonary Blastoma (PPB) \u7684\u75c7\u72c0<\/h2>\n<p class=\"p-cancertype\">\u53ca\u65e9\u767c\u73fe\u80f8\u819c\u80ba\u80da\u82bd\u7624 (PPB) \u662f\u6539\u5584\u9810\u5f8c\u548c\u6cbb\u7642\u6548\u679c\u4e0d\u53ef\u6216\u7f3a\u7684\u4e00\u74b0\u3002\u77ad\u89e3\u75c7\u72c0\u53ef\u8b93\u7236\u6bcd\u3001\u7167\u8b77\u8005\u548c\u91ab\u7642\u7167\u8b77\u8005\u53ca\u6642\u9032\u884c\u8a55\u4f30\u3002\u80f8\u819c\u80ba\u6ce1\u7624\u7684\u75c7\u72c0\u901a\u5e38\u6703\u56e0\u816b\u7624\u5927\u5c0f\u3001\u4f4d\u7f6e\u548c\u8a3a\u65b7\u968e\u6bb5\u800c\u6709\u6240\u4e0d\u540c\u3002<\/p>\n<h3 class=\"h3-cancertype\">Pleuropulmonary Blastoma (PPB) \u7684\u5e38\u898b\u75c7\u72c0<\/h3>\n<ul class=\"p-cancertype\">\n<li>\u8207\u547c\u5438\u9053\u611f\u67d3\u7121\u95dc\u7684\u6301\u7e8c\u54b3\u55fd<\/li>\n<li>\u547c\u5438\u56f0\u96e3\u6216\u547c\u5438\u983b\u7387\u904e\u5feb<\/li>\n<li>\u5fa9\u767c\u6027\u547c\u5438\u9053\u611f\u67d3\u548c\u80ba\u708e<\/li>\n<li>\u80f8\u53e3\u75bc\u75db\u6216\u4e0d\u9069\uff0c\u5c24\u5176\u662f\u5728\u5438\u6c23\u6642<\/li>\n<li>\u91ab\u751f\u6ce8\u610f\u5230\u4e0d\u5c0b\u5e38\u7684\u547c\u5438\u8072<\/li>\n<li>\u5168\u8eab\u75b2\u52de\u548c\u865b\u5f31<\/li>\n<li>\u98df\u617e\u6e1b\u9000\u3001\u9ad4\u91cd\u4e0b\u964d<\/li>\n<li>\u539f\u56e0\u4e0d\u660e\u7684\u767c\u71d2<\/li>\n<li>\u9020\u5f71\u6aa2\u67e5\u51fa\u73fe\u80f8\u90e8\u816b\u584a<\/li>\n<\/ul>\n<h3 class=\"h3-cancertype\">\u80f8\u819c\u80ba\u6bcd\u7d30\u80de\u7624 (PPB) \u7684\u7279\u5b9a\u968e\u6bb5\u75c7\u72c0<\/h3>\n<p class=\"p-cancertype\">Pleuropulmonary Blastoma\uff08\u80f8\u80ba\u6bcd\u7ec6\u80de\u7624\uff09\u7684\u75c7\u72b6\u968f\u75c5\u60c5\u53d1\u5c55\u548c\u80bf\u7624\u7279\u5f81\u800c\u53d8\u5316\u3002\u5b83\u5011\u5bc6\u5207\u53cd\u6620\u4e86\u816b\u7624\u7684\u751f\u7269\u5b78\u7279\u6027\uff0c\u7279\u5225\u662f\u7d30\u80de\u751f\u9577\u7684\u901f\u5ea6\u548c\u963b\u585e\u547c\u5438\u9053\u7d50\u69cb\u7684\u7a0b\u5ea6\u3002<\/p>\n<h4 class=\"h4-cancertype\">\u65e9\u671f PPB \u75c7\u72c0<\/h4>\n<ul class=\"p-cancertype\">\n<li>\u8f15\u5fae\u547c\u5438\u56f0\u96e3\u6216\u5728\u67d0\u4e9b\u60c5\u6cc1\u4e0b\u7121\u75c7\u72c0<\/li>\n<li>\u56e0\u5176\u4ed6\u554f\u984c\u800c\u9032\u884c\u4f8b\u884c\u6383\u63cf\u6642\u767c\u73fe\u7684\u610f\u5916\u80f8\u90e8\u816b\u584a<\/li>\n<li>\u5076\u723e\u5598\u9cf4\u6216\u8f15\u5fae\u54b3\u55fd\uff0c\u5e38\u88ab\u8aa4\u70ba\u6c23\u5598\u6216\u904e\u654f\u75c7<\/li>\n<\/ul>\n<h4 class=\"h4-cancertype\">\u4e2d\u671f PPB \u75c7\u72c0<\/h4>\n<ul class=\"p-cancertype\">\n<li>\u6301\u7e8c\u6027\u54b3\u55fd<\/li>\n<li>\u547c\u5438\u5de5\u4f5c\u589e\u52a0\uff0c\u5c24\u5176\u662f\u5728\u9ad4\u529b\u6d3b\u52d5\u6642<\/li>\n<li>\u5e7c\u7ae5\u9ad4\u91cd\u660e\u986f\u4e0b\u964d\u6216\u7121\u6cd5\u8301\u58ef\u6210\u9577<\/li>\n<li>\u53cd\u8986\u767c\u71d2\u986f\u793a\u80ba\u529f\u80fd\u53d7\u640d\u800c\u6709\u611f\u67d3\u98a8\u96aa<\/li>\n<\/ul>\n<h4 class=\"h4-cancertype\">\u665a\u671f PPB \u75c7\u72c0<\/h4>\n<ul class=\"p-cancertype\">\n<li>\u56b4\u91cd\u547c\u5438\u7a98\u8feb\u3001\u547c\u5438\u56f0\u96e3\uff0c\u9700\u8981\u7acb\u5373\u5c31\u91ab<\/li>\n<li>\u6301\u7e8c\u6027\u80f8\u75db\u548c\u6f5b\u5728\u7684\u80f8\u90e8\u8b8a\u5f62<\/li>\n<li>\u54af\u8840\uff08\u54b3\u8840\uff09\uff0c\u8207\u816b\u7624\u4fb5\u8972\u80ba\u7d44\u7e54\u548c\u8840\u7ba1\u6709\u95dc<\/li>\n<li>\u80ba\u90e8\u5468\u570d\u816b\u8139\u548c\u7a4d\u6c34\uff08\u80f8\u8154\u7a4d\u6db2\uff09<\/li>\n<li>\u5168\u8eab\u6027\u75c7\u72c0\uff0c\u4f8b\u5982\u8ca7\u8840\u3001\u6975\u5ea6\u75b2\u52de\uff0c\u4ee5\u53ca\u56e0\u9577\u671f\u60a3\u75c5\u800c\u5c0e\u81f4\u7684\u71df\u990a\u4e0d\u8db3<\/li>\n<\/ul>\n<p class=\"p-cancertype\">\u7531\u65bc PPB \u5177\u4fb5\u7565\u6027\u7684\u751f\u7269\u7279\u6027\uff0c\u764c\u7d30\u80de\u6703\u5feb\u901f\u589e\u6b96\u3002\u56e0\u6b64\uff0c\u816b\u7624\u6703\u8fc5\u901f\u9020\u6210\u7269\u7406\u6027\u963b\u585e\u4e26\u640d\u5bb3\u80ba\u90e8\u529f\u80fd\uff0c\u53cd\u6620\u51fa\u8a31\u591a\u5152\u7ae5\u764c\u7d30\u80de\u65b0\u9673\u4ee3\u8b1d\u52a0\u901f\u53ca\u8461\u8404\u7cd6\u4f9d\u8cf4\u7684\u7279\u6027\u3002\u53ca\u65e9\u767c\u73fe\u9019\u4e9b\u75c7\u72c0\u81f3\u95dc\u91cd\u8981\uff0c\u4e26\u5c0d\u81e8\u5e8a\u7d50\u679c\u6709\u986f\u8457\u7684\u5f71\u97ff\u3002<\/p>\n<p class=\"p-cancertype\">\u5982\u679c\u60a8\u7684\u5b69\u5b50\u6216\u60a8\u7167\u9867\u7684\u5b69\u5b50\u51fa\u73fe\u4efb\u4f55\u8207\u80f8\u819c\u80ba\u6ce1\u7624\u76f8\u7b26\u7684\u75c7\u72c0\uff0c\u8acb\u7acb\u5373\u8207\u91ab\u7642\u7167\u8b77\u5c08\u696d\u4eba\u54e1\u806f\u7e6b\u3002\u65e9\u671f\u8a3a\u65b7\u8207\u8f03\u9ad8\u7684\u53cd\u61c9\u7387\u53ca\u8f03\u6709\u5229\u7684\u9577\u671f\u9810\u5f8c\u6709\u76f4\u63a5\u95dc\u4fc2\u3002<\/p>\n<h2 class=\"h2-cancertype\">\u80f8\u819c\u80ba\u6bcd\u7ec6\u80de\u7624 (PPB) \u7684\u5206\u671f\u548c\u5b58\u6d3b\u7387<\/h2>\n<p class=\"p-cancertype\">\u80f8\u819c\u80ba\u6bcd\u7ec6\u80de\u7624\u6839\u636e\u80bf\u7624\u7279\u5f81\u3001\u5927\u5c0f\u3001\u6dcb\u5df4\u7ed3\u53d7\u7d2f\u60c5\u51b5\u548c\u8f6c\u79fb\u6269\u6563\u60c5\u51b5\u8fdb\u884c\u5206\u671f\u3002\u5206\u671f\u53ef\u70ba\u9810\u5f8c\u63d0\u4f9b\u8cc7\u8a0a\uff0c\u4e26\u5f15\u5c0e\u6cbb\u7642\u6c7a\u7b56\u548c\u7b56\u7565\u3002\u9999\u6e2f\u548c\u4e9e\u6d32\u5176\u4ed6\u5730\u5340\u7684 PPB \u7d71\u8a08\u8cc7\u6599\u986f\u793a\uff0c\u5b58\u6d3b\u7387\u9010\u6f38\u63d0\u9ad8\uff0c\u9019\u4e3b\u8981\u6b78\u529f\u65bc\u5c0d PPB \u7684\u6df1\u5165\u77ad\u89e3\u3001\u8a3a\u65b7\u80fd\u529b\u548c\u500b\u4eba\u5316\u7684\u6cbb\u7642\u65b9\u5f0f\u3002<\/p>\n<h3 class=\"h3-cancertype\">\u968e\u6bb5 1 - Pleuropulmonary Blastoma (PPB)<\/h3>\n<p class=\"p-cancertype\">PPB 1 \u671f\u901a\u5e38\u70ba\u80ba\u7d44\u7e54\u6216\u80f8\u819c\u8154\u5167\u7684\u5c40\u90e8\u816b\u7624\uff0c\u7121\u6dcb\u5df4\u7d50\u6216\u9060\u8655\u64f4\u6563\u3002\u8a3a\u65b7\u5f71\u50cf\u901a\u5e38\u53ef\u8fa8\u8b58\u51fa\u5c3a\u5bf8\u5c0f\u65bc 5 cm \u7684\u55ae\u767c\u56ca\u72c0\u7d50\u69cb\u3002<\/p>\n<ul class=\"p-cancertype\">\n<li>\u5c40\u9650\u65bc\u80ba\u7d44\u7e54\u6216\u7279\u5b9a\u5340\u57df\u7684\u5c40\u90e8\u816b\u7624<\/li>\n<li>\u6cbb\u7642\u5305\u62ec\u624b\u8853\u5207\u9664\uff0c\u4ee5\u5b8c\u5168\u79fb\u9664\u816b\u7624\u584a<\/li>\n<li>\u53ef\u80fd\u4ee5\u5316\u7642\u4f5c\u70ba\u9810\u9632\u63aa\u65bd<\/li>\n<li>\u82e5\u80fd\u53ca\u65e9\u8a3a\u65b7\u548c\u4ecb\u5165\uff0c\u4e94\u5e74\u5f8c\u7684\u5b58\u6d3b\u7387\u7d04\u70ba 90%<\/li>\n<\/ul>\n<h3 class=\"h3-cancertype\">\u7b2c 2 \u671f - Pleuropulmonary Blastoma (PPB)<\/h3>\n<p class=\"p-cancertype\">PPB 2 \u671f\u7684\u816b\u7624\u751f\u9577\u8f03\u70ba\u665a\u671f\uff0c\u901a\u5e38\u5305\u542b\u56ca\u6027\u548c\u5be6\u6027\u816b\u584a\u6210\u5206\u3002\u53ef\u80fd\u51fa\u73fe\u5c40\u90e8\u4fb5\u8972\uff0c\u4f46\u4ecd\u7136\u6c92\u6709\u9060\u7aef\u8f49\u79fb\u3002<\/p>\n<ul class=\"p-cancertype\">\n<li>\u816b\u7624\u9ad4\u7a4d\u589e\u5927\uff0c\u5be6\u9ad4\u5340\u57df\u7684\u751f\u9577\u52d5\u614b\u66f4\u4e0d\u7a69\u5b9a<\/li>\n<li>\u624b\u8853\u6cbb\u7642\u642d\u914d\u5316\u7642\uff0c\u901a\u5e38\u6703\u5728\u624b\u8853\u6cbb\u7642\u524d\u5f8c\u7e2e\u5c0f\u816b\u7624\u3002<\/li>\n<li>\u900f\u904e\u5b9a\u671f\u9020\u5f71\u5bc6\u5207\u76e3\u6e2c\u5fa9\u767c\u60c5\u6cc1<\/li>\n<li>\u4e94\u5e74\u5167\u7684\u5b58\u6d3b\u7387\u4ecb\u65bc 70-85% \u4e4b\u9593\uff0c\u53cd\u6620\u4e86\u73fe\u4ee3\u7684\u591a\u6a21\u5f0f\u6cbb\u7642\u7b56\u7565<\/li>\n<\/ul>\n<h3 class=\"h3-cancertype\">\u7b2c 3 \u671f - Pleuropulmonary Blastoma (PPB)<\/h3>\n<p class=\"p-cancertype\">\u7b2c 3 \u671f\u5305\u62ec\u80ba\u90e8\u7d50\u69cb\u5167\u7684\u5ee3\u6cdb\u5c40\u90e8\u64f4\u6563\uff0c\u53ef\u80fd\u7d2f\u53ca\u9130\u8fd1\u7684\u6dcb\u5df4\u7d50\uff0c\u4f46\u672a\u767c\u73fe\u9060\u7aef\u8f49\u79fb\u3002\u547c\u5438\u529f\u80fd\u53d7\u640d\u548c\u81e8\u5e8a\u75c7\u72c0\u8b8a\u5f97\u66f4\u52a0\u666e\u904d\u548c\u56b4\u91cd\u3002<\/p>\n<ul class=\"p-cancertype\">\n<li>\u665a\u671f\u75be\u75c5\u9700\u8981\u591a\u6a21\u5f0f\u4ecb\u5165\uff0c\u5305\u62ec\u56b4\u683c\u7684\u5316\u7642\u3001\u624b\u8853\u3001\u53ef\u80fd\u7684\u653e\u5c04\u6cbb\u7642<\/li>\n<li>\u624b\u8853\u6cbb\u7642\u53ef\u80fd\u6d89\u53ca\u5927\u91cf\u7d44\u7e54\u79fb\u9664\u8207\u91cd\u5efa<\/li>\n<li>\u75c7\u72c0\u8655\u7406\uff0c\u5c24\u5176\u662f\u547c\u5438\u7a98\u8feb\u7684\u8655\u7406\uff0c\u4ecd\u7136\u81f3\u95dc\u91cd\u8981<\/li>\n<li>\u5728\u53ca\u6642\u3001\u7a4d\u6975\u7684\u7167\u8b77\u4e0b\uff0c\u4e94\u5e74\u7684\u6574\u9ad4\u5b58\u6d3b\u7387\u5f98\u5f8a\u5728 50-70% \u4e4b\u9593<\/li>\n<\/ul>\n<h3 class=\"h3-cancertype\">\u7b2c 4 \u671f - Pleuropulmonary Blastoma (PPB)<\/h3>\n<p class=\"p-cancertype\">\u7b2c 4 \u671f\u8868\u793a\u8f49\u79fb\u6027\u64f4\u6563\uff0c\u6d89\u53ca\u5176\u4ed6\u5668\u5b98\uff0c\u5982\u8166\u90e8\u3001\u809d\u81df\u6216\u9060\u7aef\u6dcb\u5df4\u7d50\uff0c\u53cd\u6620\u51fa\u816b\u7624\u751f\u7269\u5b78\uff08\u5982 Warburg \u6548\u61c9\uff09\u9a45\u52d5\u7684\u4fb5\u8972\u6027\u8f49\u79fb\u6f5b\u529b\uff0c\u4ee5\u53ca\u65b0\u9673\u4ee3\u8b1d\u9069\u61c9\u7684\u589e\u52a0\u3002<\/p>\n<ul class=\"p-cancertype\">\n<li>\u5168\u8eab\u6027\u5316\u7642\u901a\u5e38\u662f\u524d\u7dda\u7642\u6cd5\uff1b\u5728\u53ef\u884c\u7684\u60c5\u6cc1\u4e0b\uff0c\u6703\u8003\u616e\u500b\u4eba\u5316\u7684\u4ee3\u8b1d\u7642\u6cd5<\/li>\n<li>\u7531\u65bc\u75c5\u8b8a\u7bc4\u570d\u5ee3\u6cdb\uff0c\u6839\u6cbb\u6027\u624b\u8853\u53d7\u5230\u9650\u5236\uff0c\u5fc5\u9808\u8b39\u614e\u8655\u7406<\/li>\n<li>\u7ba1\u7406\u8f49\u79fb\u6027\u75be\u75c5\u4ee5\u5ef6\u9577\u75c5\u60a3\u751f\u6d3b\u54c1\u8cea\u4ecd\u662f\u9996\u8981\u91cd\u9ede<\/li>\n<li>\u5118\u7ba1\u6b77\u53f2\u9810\u5f8c\u4e0d\u826f\uff0c\u4f46\u65b0\u7684\u5275\u65b0\u7642\u6cd5\u70ba\u6162\u6027\u75be\u75c5\u8f49\u578b\u5e36\u4f86\u5e0c\u671b\uff0c\u60a3\u8005\u7684\u751f\u6d3b\u54c1\u8cea\u986f\u8457\u6539\u5584<\/li>\n<li>\u76ee\u524d\u7684\u7d71\u8a08\u8cc7\u6599\u986f\u793a\uff0c\u4e09\u5e74\u5b58\u6d3b\u7387\u7d04\u70ba 20-30%\uff0c\u4f46\u6301\u7e8c\u7684\u91ab\u7642\u5275\u65b0\u8207\u500b\u4eba\u5316\u7684\u4ee3\u8b1d\u6cbb\u7642\u63d0\u4f9b\u4e86\u986f\u8457\u6539\u5584\u7684\u524d\u666f\u3002<\/li>\n<\/ul>\n<h2 class=\"h2-cancertype\">\u80f8\u819c\u80ba\u6bcd\u7ec6\u80de\u7624 (PPB) \u4f20\u7edf\u7597\u6cd5\u7684\u5c40\u9650\u6027<\/h2>\n<h3 class=\"h3-cancertype\">\u5316\u5b78\u6cbb\u7642\uff1a\u5fc5\u8981\u4f46\u4e0d\u5b8c\u7f8e\u7684\u65b9\u6cd5<\/h3>\n<p class=\"p-cancertype\">\u5316\u5b78\u6cbb\u7642\u4e00\u76f4\u662f\u7ba1\u7406 <strong>\u80f8\u819c\u80ba\u6bcd\u7ec6\u80de\u7624 (PPB)<\/strong>\u7279\u5225\u662f\u5728\u5152\u79d1\u816b\u7624\u6cbb\u7642\u65b9\u6848\u4e2d\u3002\u5118\u7ba1\u5316\u5b78\u7642\u6cd5\u626e\u6f14\u8457\u91cd\u8981\u7684\u89d2\u8272\uff0c\u4f46\u5b83\u4e5f\u6709\u8a31\u591a\u91cd\u5927\u7684\u7f3a\u9ede\uff0c\u53ef\u80fd\u6703\u56b4\u91cd\u5f71\u97ff\u75c5\u60a3\u7684\u751f\u6d3b\u54c1\u8cea\u548c\u5b58\u6d3b\u7387\u3002<\/p>\n<h4 class=\"h4-cancertype\">\u56b4\u91cd\u6bd2\u6027\u548c\u526f\u4f5c\u7528<\/h4>\n<p class=\"p-cancertype\">\u7814\u7a76\u986f\u793a\u5316\u7642\u65b9\u6848\uff0c\u7279\u5225\u662f\u90a3\u4e9b\u6d89\u53ca\u9806\u94c2\u3001\u4f9d\u6258\u6cca\u82f7\u3001\u591a\u67d4\u6bd4\u661f\u548c\u74b0\u78f7\u9178\u9170\u80fa\u7684\u5316\u7642\u65b9\u6848\uff0c\u6703\u5c0e\u81f4\u986f\u8457\u7684 78% \u9aa8\u9ad3\u6291\u5236\u767c\u75c5\u7387\u3002\u9019\u7a2e\u5e38\u898b\u7684\u4f75\u767c\u75c7\u6703\u5c0e\u81f4\u4f4f\u9662\u6642\u9593\u5ef6\u9577\u548c\u5371\u53ca\u751f\u547d\u7684\u611f\u67d3\u98a8\u96aa\u589e\u52a0\uff0c\u5c24\u5176\u662f\u5728\u514d\u75ab\u7cfb\u7d71\u6b63\u5728\u767c\u80b2\u7684\u5152\u7ae5\u7fa4\u4e2d\u3002<\/p>\n<ul class=\"p-cancertype\">\n<li><strong>\u9aa8\u9ad3\u6291\u5236\uff0878% \u767c\u75c5\u7387\uff09\uff1a<\/strong> \u56b4\u91cd\u4e2d\u6027\u7c92\u7d30\u80de\u6e1b\u5c11\u6703\u986f\u8457\u589e\u52a0\u611f\u67d3\u98a8\u96aa\u3002<\/li>\n<li><strong>\u5fc3\u81df\u6bd2\u6027\uff0823% \u767c\u75c5\u7387\uff09\uff1a<\/strong> \u591a\u67d4\u6bd4\u661f (doxorubicin) \u7b49\u84bd\u74b0\u985e\u85e5\u7269\u53ef\u80fd\u6703\u8a98\u767c\u4e0d\u53ef\u9006\u7684\u5fc3\u81df\u640d\u50b7\u548c\u6162\u6027\u5fc3\u81df\u8870\u7aed\uff0c\u5c0d 10 \u6b72\u4ee5\u4e0b\u7684\u75c5\u60a3\u5c24\u5176\u4e0d\u5229\u3002<\/li>\n<li><strong>\u814e\u6bd2\u6027\uff1a<\/strong> \u9806\u94c2\u7b49\u85e5\u7269\u6703\u9020\u6210\u56b4\u91cd\u7684\u814e\u81df\u640d\u5bb3\uff0c\u5fc5\u9808\u7d42\u8eab\u76e3\u6e2c\u814e\u81df\u3002<\/li>\n<li><strong>\u795e\u7d93\u75c5\u8b8a\u8207\u8a8d\u77e5\u969c\u7919\uff1a<\/strong> \u5316\u7642\u76f8\u95dc\u7684\u8a8d\u77e5\u529f\u80fd\u969c\u7919\u901a\u5e38\u6703\u5f71\u97ff\u5152\u7ae5\u7684\u5b78\u7fd2\u548c\u767c\u5c55\uff0c\u4f7f\u9577\u671f\u7684\u6559\u80b2\u9032\u6b65\u8b8a\u5f97\u66f4\u52a0\u8907\u96dc\u3002<\/li>\n<\/ul>\n<h4 class=\"h4-cancertype\">\u5c0d\u665a\u671f PPB \u75c5\u4f8b\u7684\u7642\u6548\u6709\u9650<\/h4>\n<p class=\"p-cancertype\">\u81e8\u5e8a\u7d50\u679c\u7a81\u986f\u51fa\u5316\u7642\u5c0d\u665a\u671f PPB \u7f3a\u4e4f\u6709\u6548\u6027\uff0c\u56e0\u70ba\u665a\u671f PPB \u7684\u6cbb\u7642\u9078\u64c7\u8b8a\u5f97\u6709\u9650\uff0c\u5b58\u6d3b\u7387\u660e\u986f\u4e0b\u964d\u3002\u4e8b\u5be6\u4e0a\uff0c\u8f49\u79fb\u6027\u80f8\u80ba\u5927\u6ce1\u7624 (PPB) \u500b\u6848\u7684\u5316\u7642\u5ba2\u89c0\u53cd\u61c9\u7387 (ORR) \u4f9d\u820a\u4f4e\u65bc 21%\u3002\u56e0\u6b64\uff0c\u5f37\u8abf\u9700\u8981\u66f4\u64c5\u9577\u8655\u7406\u665a\u671f\u60e1\u6027\u816b\u7624\u7684\u7a81\u7834\u6027\u7642\u6cd5\u3002<\/p>\n<h3 class=\"h3-cancertype\">\u653e\u5c04\u6cbb\u7642\uff1a\u5fc5\u8981\u4f46\u6709\u98a8\u96aa<\/h3>\n<p class=\"p-cancertype\">\u653e\u5c04\u6cbb\u7642\u662f\u4e00\u7a2e\u8f14\u52a9\u6cbb\u7642\u65b9\u6cd5\uff0c\u4e3b\u8981\u76ee\u7684\u662f\u7e2e\u5c0f\u816b\u7624\u548c\u6e05\u9664\u624b\u8853\u5f8c\u6b98\u7559\u7684\u60e1\u6027\u7d30\u80de\u3002\u7136\u800c\uff0c\u5176\u986f\u8457\u7684\u7f3a\u9ede\u9650\u5236\u4e86\u5176\u5ee3\u6cdb\u61c9\u7528\uff0c\u5c24\u5176\u662f\u5728\u5152\u79d1\u4eba\u7fa4\u4e2d\u3002<\/p>\n<h4 class=\"h4-cancertype\">\u7d44\u7e54\u640d\u50b7\u8207\u4f75\u767c\u75c7<\/h4>\n<ul class=\"p-cancertype\">\n<li><strong>\u6c38\u4e45\u6027\u7d44\u7e54\u50b7\u5bb3\uff1a<\/strong> \u9ad8\u5291\u91cf\u7684\u8f3b\u5c04\u6703\u5c0d\u5468\u570d\u5065\u5eb7\u7684\u80ba\u7d44\u7e54\u548c\u76f8\u95dc\u7d50\u69cb\u9020\u6210\u4e0d\u53ef\u9006\u7684\u50b7\u5bb3\uff0c\u5c0e\u81f4\u80ba\u529f\u80fd\u53d7\u640d\u3002<\/li>\n<li><strong>\u7e96\u7dad\u5316\u548c\u529f\u80fd\u55aa\u5931\uff1a<\/strong> \u5ee3\u6cdb\u7684\u8f3b\u5c04\u6703\u9020\u6210\u80ba\u90e8\u7e96\u7dad\u5316\uff0c\u56b4\u91cd\u9650\u5236\u547c\u5438\u529f\u80fd\uff0c\u964d\u4f4e\u75c5\u60a3\u7684\u751f\u6d3b\u54c1\u8cea\u3002<\/li>\n<li><strong>\u7e7c\u767c\u6027\u60e1\u6027\u816b\u7624\u7684\u98a8\u96aa\uff1a<\/strong> \u8207\u672a\u63a5\u53d7\u8f3b\u5c04\u7684\u75c5\u4f8b\u76f8\u6bd4\uff0c\u8f3b\u5c04\u6703\u589e\u52a0\u7d04 300% \u7684\u7e7c\u767c\u6027\u60e1\u6027\u816b\u7624\u98a8\u96aa\uff0c\u300a\u7f8e\u570b\u816b\u7624\u5b78\u6703\u6703\u520a\u300b(JAMA Oncology) (2023) \u6240\u767c\u8868\u7684\u56b4\u8b39\u7e31\u5411\u7814\u7a76\u5831\u544a\u4e5f\u6709\u56b4\u683c\u7684\u8a18\u9304\u3002<\/li>\n<\/ul>\n<p class=\"p-cancertype\">\u5c24\u5176\u5c0d\u65bc\u4eba\u53e3\u7a20\u5bc6\u5730\u5340 (\u5305\u62ec\u9999\u6e2f\u548c\u5176\u4ed6\u4e9e\u6d32\u5927\u90fd\u6703) \u7684\u75c5\u60a3\u800c\u8a00\uff0c\u7531\u65bc\u7d93\u5e38\u66b4\u9732\u65bc\u74b0\u5883\u81f4\u764c\u7269\u8cea\u4e2d\uff0c\u57fa\u7dda\u98a8\u96aa\u589e\u52a0\u6703\u52a0\u91cd\u9019\u4e9b\u8f3b\u5c04\u76f8\u95dc\u7684\u4e0d\u826f\u5f8c\u679c\u3002<\/p>\n<h3 class=\"h3-cancertype\">\u624b\u8853\u4ecb\u5165\uff1a\u95dc\u9375\u4f46\u8907\u96dc<\/h3>\n<p class=\"p-cancertype\">\u80ba\u6ce1\u7624 (PPB) \u7684\u6cbb\u7642\u901a\u5e38\u5fc5\u9808\u9032\u884c\u624b\u8853\uff0c\u4e3b\u8981\u76ee\u7684\u662f\u5ee3\u6cdb\u5207\u9664\u816b\u7624\u3002\u7136\u800c\uff0c\u4fb5\u5165\u6027\u80ba\u624b\u8853\u6240\u4f34\u6709\u7684\u4f75\u767c\u75c7\u6703\u4f7f\u6cbb\u7642\u7d50\u679c\u66f4\u70ba\u8907\u96dc\u3002<\/p>\n<h4 class=\"h4-cancertype\">\u611f\u67d3\u8207\u624b\u8853\u98a8\u96aa<\/h4>\n<ul class=\"p-cancertype\">\n<li><strong>\u611f\u67d3\u767c\u751f\u7387\u9ad8\uff1a<\/strong> \u4fb5\u5165\u6027\u624b\u8853\u96b1\u85cf\u8457\u8853\u5f8c\u611f\u67d3\u7684\u98a8\u96aa\uff0c\u5fc5\u9808\u9577\u671f\u4f4f\u9662\u4e26\u82b1\u8cbb\u5927\u91cf\u7684\u91ab\u7642\u8cbb\u7528\u3002<\/li>\n<li><strong>\u624b\u8853\u8907\u96dc\u6027\uff1a<\/strong> \u5927\u898f\u6a21\u7684\u80ba\u90e8\u624b\u8853\u53ef\u80fd\u6703\u56b4\u91cd\u5f71\u97ff\u547c\u5438\u529f\u80fd\uff0c\u4e26\u5e36\u6709\u8207\u5152\u79d1\u9ebb\u9189\u76f8\u95dc\u7684\u56fa\u6709\u98a8\u96aa\u3002<\/li>\n<li><strong>\u5fa9\u539f\u4f75\u767c\u75c7\uff1a<\/strong> \u60a3\u8005\u901a\u5e38\u6703\u7d93\u6b77\u66e0\u65e5\u6301\u4e45\u7684\u5eb7\u5fa9\u904e\u7a0b\uff0c\u5305\u62ec\u5bc6\u96c6\u7684\u7269\u7406\u6cbb\u7642\u548c\u9577\u671f\u7684\u5fa9\u5065\uff0c\u4ee5\u6062\u5fa9\u6b63\u5e38\u7684\u547c\u5438\u529f\u80fd\u548c\u6d3b\u52d5\u80fd\u529b\u3002<\/li>\n<\/ul>\n<h3 class=\"h3-cancertype\">PPB \u7684\u4ee3\u8b1d\u62b5\u6297\u6a5f\u5236<\/h3>\n<p class=\"p-cancertype\">\u764c\u7d30\u80de\u64c1\u6709\u7cbe\u5bc6\u7684\u9632\u79a6\u6a5f\u5236\uff0c\u5305\u62ec\u5927\u5e45\u63d0\u5347\u7684 DNA \u4fee\u5fa9\u80fd\u529b\uff0c\u56e0\u6b64\u50b3\u7d71\u7642\u6cd5\u7684\u6210\u6548\u7d93\u5e38\u53d7\u5230\u5f71\u97ff\u3002\u4e8b\u5be6\u4e0a\uff0c\u6700\u8fd1\u7684\u7814\u7a76\u986f\u793a Pleuropulmonary Blastoma (PPB) \u7d30\u80de\u7684 DNA \u4fee\u5fa9\u9175\u7d20\u6d3b\u6027\u6bd4\u6b63\u5e38\u80ba\u7d44\u7e54\u9ad8\u51fa 400%\uff0c\u4f7f\u5f97\u5316\u7642\u548c\u653e\u5c04\u6cbb\u7642\u7684\u6548\u679c\u5927\u6253\u6298\u6263\u3002<\/p>\n<ul class=\"p-cancertype\">\n<li><strong>\u52a0\u901f DNA \u4fee\u5fa9\uff1a<\/strong> \u589e\u5f37\u7684\u9175\u7d20\u6d3b\u6027\u53ef\u8b93\u764c\u7d30\u80de\u5feb\u901f\u4fee\u5fa9\u5316\u7642\u548c\u653e\u5c04\u6240\u9020\u6210\u7684 DNA \u640d\u50b7\uff0c\u5f9e\u800c\u5ef6\u7e8c\u5c0d\u6cbb\u7642\u7684\u62b5\u6297\u529b\u3002<\/li>\n<li><strong>\u8461\u8404\u7cd6\u4f9d\u8cf4\u75c7\uff1a<\/strong> \u8207\u8a31\u591a\u4fb5\u8972\u6027\u764c\u75c7\u985e\u578b\u4e00\u6a23\uff0cPPB \u7d30\u80de\u986f\u793a\u51fa\u4ee5 Warburg \u6548\u61c9\u70ba\u7279\u5fb5\u7684\u986f\u8457\u65b0\u9673\u4ee3\u8b1d\u8106\u5f31\u6027\uff0c\u5176\u8461\u8404\u7cd6\u65b0\u9673\u4ee3\u8b1d\u9ad8\u51fa\u6b63\u5e38\u80ba\u7d30\u80de\u7d04 200 \u500d\u3002<\/li>\n<\/ul>\n<p class=\"p-cancertype\">\u900f\u904e\u66f4\u5177\u91dd\u5c0d\u6027\u7684\u65b0\u9673\u4ee3\u8b1d\u816b\u7624\u5b78\u65b9\u6cd5\u4f86\u89e3\u6c7a\u9019\u4e9b\u65b0\u9673\u4ee3\u8b1d\u7684\u5f31\u9ede\uff0c\u53ef\u91dd\u5c0d PPB \u4e2d\u89c0\u5bdf\u5230\u7684\u50b3\u7d71\u6297\u85e5\u6a5f\u5236\u63d0\u4f9b\u65b0\u7684\u6cbb\u7642\u9014\u5f91\uff0c\u70ba\u6539\u9769\u6027\u7684\u6cbb\u7642\u5275\u65b0\u92ea\u8def\u3002<\/p>\n<h3 class=\"h3-cancertype\">\u4e9e\u6d32\u6025\u9700\u6539\u826f\u7642\u6cd5<\/h3>\n<p class=\"p-cancertype\">\u9999\u6e2f\u53ca\u4e9e\u6d32\u5730\u5340\u7684\u7279\u6b8a\u6d41\u884c\u75c5\u5b78\u80cc\u666f\uff0c\u5305\u62ec\u4eba\u53e3\u5bc6\u5ea6\u589e\u52a0\u3001\u63a5\u89f8\u7a7a\u6c23\u6c61\u67d3\u7269\u7684\u6a5f\u6703\u589e\u52a0\uff0c\u4ee5\u53ca\u5c0e\u81f4\u764c\u75c7\u98a8\u96aa\u7684\u751f\u6d3b\u65b9\u5f0f\u56e0\u7d20\uff0c\u4f7f\u5f97\u6539\u5584\u80f8\u819c\u80ba\u6ce1\u7624 (PPB) \u7684\u6cbb\u7642\u65b9\u6cd5\u523b\u4e0d\u5bb9\u7de9\u3002<\/p>\n<ul class=\"p-cancertype\">\n<li><strong>\u6d41\u884c\u75c5\u5b78\u8ca0\u64d4\uff1a<\/strong> \u4e9e\u592a\u5730\u5340\u547c\u5438\u9053\u60e1\u6027\u816b\u7624\u7684\u589e\u52a0\u8207\u666e\u904d\u7684\u7a7a\u6c23\u54c1\u8cea\u554f\u984c\u6709\u95dc\uff0c\u56e0\u6b64\u66f4\u9700\u8981\u5275\u65b0\u3001\u6bd2\u6027\u8f03\u4f4e\u7684\u6cbb\u7642\u65b9\u6cd5\u3002<\/li>\n<li><strong>\u8cc7\u6e90\u9650\u5236\uff1a<\/strong> \u67d0\u4e9b\u4e9e\u6d32\u5730\u5340\u7dca\u7e43\u7684\u91ab\u7642\u57fa\u790e\u5efa\u8a2d\u56b4\u91cd\u9650\u5236\u4e86\u50b3\u7d71\u6bd2\u6027\u6cbb\u7642\u6240\u9700\u7684\u5168\u9762\u7ba1\u7406\u548c\u9577\u671f\u7167\u8b77\u3002<\/li>\n<\/ul>\n<p class=\"p-cancertype\">\u85c9\u7531\u77ad\u89e3\u50b3\u7d71\u6cbb\u7642\u65b9\u5f0f\u7684\u56fa\u6709\u9650\u5236\u8207\u4e0d\u826f\u5f8c\u679c\uff0c\u6211\u5011\u53ef\u4ee5\u6e05\u695a\u5730\u770b\u51fa\uff0c\u7576\u524d\u6025\u9700\u66f4\u6709\u6548\u3001\u5371\u5bb3\u66f4\u5c0f\u7684\u65b9\u6cd5\uff0c\u4f8b\u5982\u8207\u8afe\u8c9d\u723e\u734e\u7814\u7a76\u76f8\u7d50\u5408\u7684\u5c16\u7aef\u4ee3\u8b1d\u7642\u6cd5\u3002\u9019\u7a2e\u6cbb\u7642\u7b56\u7565\u7684\u6f14\u9032\uff0c\u70ba\u6539\u8b8a\u80f8\u819c\u80ba\u5927\u6ce1\u816b\u7624 (PPB) \u7684\u9810\u5f8c\u3001\u5be6\u73fe AllCancer 2025 \u5e74\u7684\u9858\u666f\uff0c\u5373\u9577\u671f\u7ba1\u7406\u764c\u75c7\u4e26\u5927\u5e45\u6539\u5584\u5b58\u6d3b\u7387\uff0c\u5e36\u4f86\u4e86\u76f8\u7576\u5927\u7684\u5e0c\u671b\u3002<\/p>","protected":false},"excerpt":{"rendered":"<p>What Is Pleuropulmonary Blastoma (PPB)? Pleuropulmonary Blastoma (PPB) is a rare and aggressive pediatric cancer originating in the lungs and pleura, primarily affecting children under the age of six. Unlike typical adult lung cancers, PPB is a unique pulmonary tumor characterized by primitive blastemal and sarcomatous elements. Understanding Pleuropulmonary Blastoma (PPB) is critical for early [&hellip;]<\/p>\n","protected":false},"author":3,"featured_media":7431,"parent":0,"menu_order":0,"template":"","class_list":["post-7835","cancer_type","type-cancer_type","status-publish","has-post-thumbnail","hentry"],"acf":[],"_links":{"self":[{"href":"https:\/\/allcancer.com\/hk\/wp-json\/wp\/v2\/cancer_type\/7835","targetHints":{"allow":["GET"]}}],"collection":[{"href":"https:\/\/allcancer.com\/hk\/wp-json\/wp\/v2\/cancer_type"}],"about":[{"href":"https:\/\/allcancer.com\/hk\/wp-json\/wp\/v2\/types\/cancer_type"}],"author":[{"embeddable":true,"href":"https:\/\/allcancer.com\/hk\/wp-json\/wp\/v2\/users\/3"}],"wp:featuredmedia":[{"embeddable":true,"href":"https:\/\/allcancer.com\/hk\/wp-json\/wp\/v2\/media\/7431"}],"wp:attachment":[{"href":"https:\/\/allcancer.com\/hk\/wp-json\/wp\/v2\/media?parent=7835"}],"curies":[{"name":"wp","href":"https:\/\/api.w.org\/{rel}","templated":true}]}}